Cardiovascular Surgery and Interventions 2022, Vol 9, Num 3 Page(s): 194-197
Left main coronary artery osteoplasty with pulmonary autograft in a child with familial hypercholesterolemia

Berra Zümrüt Tan-Recep, Ali Can Hatemi

Department of Pediatric Cardiac Surgery, Başakşehir Çam and Sakura City Hospital, Istanbul, Türkiye

Keywords: Familial hypercholesterolemia, left main coronary osteal stenosis, pulmonary autograft
Familial hypercholesterolemia is a disease characterized by mutations in the low-density lipoprotein receptor. Total cholesterol levels >500 mg/dL and low-density lipoprotein levels >350 mg/dL are associated with early atherosclerosis. In these patients, the incidence of coronary artery disease is high in the first decade of life, and it often emerges in adolescence. Herein, we present a 14-year-old female with familial hypercholesterolemia who underwent left main coronary artery osteoplasty with a pulmonary autograft due to an incidentally detected osteal stenosis of the left main coronary artery. The patient was discharged without any problems, and no problems were detected during the follow-up.

DOI : 10.5606/e-cvsi.2022.1376